Serological diagnosis of chronic skin granulomas caused by wild-type or vaccine-derived rubella virus in patients with inherited HLA class I deficiency.

Serological diagnosis of chronic skin granulomas caused by wild-type or vaccine-derived rubella virus in patients with inherited HLA class I deficiency.

Luciani L,Darazam I,Nougairède A,Robert S,Momenilandi M,Rosain J,Bustamante J,Deswarte C,Adamski H,Picard-Dahan C,Mansouri N,Piorkowski G,Cortes A,Placidi C,Descamps V,Suarez F,Casanova J,Mansouri D,de Lamballerie X,Béziat V

Source :

2025 Jul 23

Pmid / DOI:

41531537

Abstract

Patients with TAP1/TAP2 deficiency develop rubella-associated skin granulomas due to impaired HLA-I antigen presentation. Markedly elevated rubella IgG levels may support diagnosis when PCR is unavailable. These findings also underscore the specific vulnerability of such patients to live-attenuated rubella vaccination.KEYWORDSHLA-I, Human leukocyte antigen (HLA) class 1, Rubella, TAP1, TAP2, bare lymphocytes syndrome

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