Autosomal Dominant IFN-γR1 Deficiency Presenting with both Atypical Mycobacteriosis and Tuberculosis in a BCG-Vaccinated South African Patient.

Glanzmann B,Möller M,Moncada-Velez M,Peter J,Urban M,van Helden P,Hoal E,de Villiers N,Glashoff R,Nortje R,Bustamante J,Abel L,Casanova J,Boisson-Dupuis S,Esser M,Kinnear C

Source :

J. Clin. Immunol.

2018 May 18

Pmid / DOI:

29777412

Abstract

KEYWORDSIFN-γ immunity, IFNGR1, Mendelian susceptibility to mycobacterial disease, Mycobacterium other than tuberculosis, South Africa, Ttuberculosis

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